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Neurology Neuroimmunology & Neuroinflammation
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A peer-reviewed clinical and translational neurology open access journal
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January 2023; 10 (1)

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Editor's Corner

  • Open Access
    N2 Year in Review
    Josep Dalmau, Marinos C. Dalakas, Dennis L. Kolson, Friedemann Paul, Raquel Sánchez-Valle, Scott S. Zamvil
    • Full Text
    • Full Text (PDF)

Research Articles

  • Open Access
    Comparison of Fixed and Live Cell-Based Assay for the Detection of AChR and MuSK Antibodies in Myasthenia Gravis
    Gregorio Spagni, Matteo Gastaldi, Pietro Businaro, Zeineb Chemkhi, Cinzia Carrozza, Giovanni Mascagna, Silvia Falso, Silvia Scaranzin, Diego Franciotta, Amelia Evoli, Valentina Damato
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Early-Stage Contactin-Associated Protein-like 2 Limbic EncephalitisClues for Diagnosis
    Jeanne Benoit, Sergio Muñiz-Castrillo, Alberto Vogrig, Antonio Farina, Anne-Laurie Pinto, Geraldine Picard, Veronique Rogemond, Deborah Guery, Agusti Alentorn, Dimitri Psimaras, Sylvain Rheims, Jérôme Honnorat, Bastien Joubert
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Senescent-like Blood Lymphocytes and Disease Progression in Amyotrophic Lateral Sclerosis
    Ozlem Yildiz, Johannes Schroth, Timothy Tree, Martin R. Turner, Pamela J. Shaw, Sian M. Henson, Andrea Malaspina
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Longitudinal Postvaccine SARS-CoV-2 Immunoglobulin G Titers, Memory B-Cell Responses, and Risk of COVID-19 in Multiple Sclerosis Over 1 Year
    Giulio Disanto, Alice Galante, Marco Cantu', Rosaria Sacco, Federico Mele, Jennifer Jessica Eisler, Franco Keller, Enos Bernasconi, Federica Sallusto, Chiara Zecca, Claudio Gobbi
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Neurofilament Light Chain Levels Are Predictive of Clinical Conversion in Radiologically Isolated Syndrome
    Manon Rival, Eric Thouvenot, Lucile Du Trieu de Terdonck, Sabine Laurent-Chabalier, Christophe Demattei, Ugur Uygunoglu, Giovanni Castelnovo, Mikael Cohen, Darin T. Okuda, Orhun H. Kantarci, Daniel Pelletier, Christina Azevedo, Philippe Marin, Sylvain Lehmann, Aksel Siva, Thibault Mura, Christine Lebrun-Frenay
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Effect of Estimated Blood Volume and Body Mass Index on GFAP and NfL Levels in the Serum and CSF of Patients With Multiple Sclerosis
    Yavor Yalachkov, Jan Hendrik Schäfer, Jasmin Jakob, Lucie Friedauer, Falk Steffen, Stefan Bittner, Christian Foerch, Martin Alexander Schaller-Paule
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Single-Cell Transcriptomics Identifies Brain Endothelium Inflammatory Networks in Experimental Autoimmune Encephalomyelitis
    Antoine Philippe Fournier, Olivier Tastet, Marc Charabati, Chloé Hoornaert, Lyne Bourbonnière, Wendy Klement, Sandra Larouche, Fiona Tea, Yu Chang Wang, Catherine Larochelle, Nathalie Arbour, Jiannis Ragoussis, Stephanie Zandee, Alexandre Prat
    • Abstract
    • Full Text
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  • Open Access
    Guillain-Barré Syndrome Following Zika Virus Infection Is Associated With a Diverse Spectrum of Peripheral Nerve Reactive Antibodies
    Alexander J. Davies, Cinta Lleixà, Ana M. Siles, Dawn S. Gourlay, Georgina Berridge, Wanwisa Dejnirattisai, Carolina Ramírez-Santana, Juan-Manuel Anaya, Andrew K. Falconar, Claudia M. Romero-Vivas, Lyda Osorio, Beatriz Parra, Gavin R. Screaton, Juthathip Mongkolsapaya, Roman Fischer, Carlos A. Pardo, Susan K. Halstead, Hugh J. Willison, Luis Querol, Simon Rinaldi
    • Abstract
    • Full Text
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  • Open Access
    Specific Patterns of Immune Cell Dynamics May Explain the Early Onset and Prolonged Efficacy of Cladribine TabletsA MAGNIFY-MS Substudy
    Heinz Wiendl, Klaus Schmierer, Suzanne Hodgkinson, Tobias Derfuss, Andrew Chan, Finn Sellebjerg, Anat Achiron, Xavier Montalban, Alexandre Prat, Nicola De Stefano, Frederik Barkhof, Letizia Leocani, Patrick Vermersch, Anita Chudecka, Claire Mwape, Kristina H. Holmberg, Ursula Boschert, Sanjeev Roy
    • Abstract
    • Full Text
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  • Open Access
    Kappa Free Light Chain Biomarkers Are Efficient for the Diagnosis of Multiple SclerosisA Large Multicenter Cohort Study
    Michael Levraut, Sabine Laurent-Chabalier, Xavier Ayrignac, Kévin Bigaut, Manon Rival, Sanae Squalli, Hélène Zéphir, Tifanie Alberto, Jean-David Pekar, Jonathan Ciron, Damien Biotti, Bénédicte Puissant-Lubrano, Jean-Philippe Camdessanché, Yannick Tholance, Olivier Casez, Bertrand Toussaint, Jeanne Marion, Thibault Moreau, Daniela Lakomy, Audrey Thomasset, Elisabeth Maillart, Delphine Sterlin, Aude Maurousset, Auriane Rocher, David Axel Laplaud, Edith Bigot-Corbel, Pierre-Olivier Bertho, Jean Pelletier, Joseph Boucraut, Pierre Labauge, Thierry Vincent, Jérôme De Sèze, Isabelle Jahn, Barbara Seitz-Polski, Eric Thouvenot, Christine Lebrun-Frenay
    • Abstract
    • Full Text
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  • Open Access
    Serum Levels of CXCL13 Are Associated With Teriflunomide Response in Patients With Multiple Sclerosis
    Nicolás Fissolo, Agustin Pappolla, Jordi Rio, Luisa M. Villar, Santiago Perez-Hoyos, Alex Sanchez, Lucía Gutierrez, Xavier Montalban, Manuel Comabella
    • Abstract
    • Full Text
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  • Open Access
    Serum GFAP and NfL Levels Differentiate Subsequent Progression and Disease Activity in Patients With Progressive Multiple Sclerosis
    Christian Barro, Brian C. Healy, Yanqing Liu, Shrishti Saxena, Anu Paul, Mariann Polgar-Turcsanyi, Charles R.G. Guttmann, Rohit Bakshi, Harald Kropshofer, Howard L. Weiner, Tanuja Chitnis
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Serum Neurofilament Identifies Patients With Multiple Sclerosis With Severe Focal Axonal Damage in a 6-Year Longitudinal Cohort
    Falk Steffen, Timo Uphaus, Nina Ripfel, Vinzenz Fleischer, Muriel Schraad, Gabriel Gonzalez-Escamilla, Sinah Engel, Sergiu Groppa, Frauke Zipp, Stefan Bittner
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Sustained Low Relapse Rate With Highly Variable B-Cell Repopulation Dynamics With Extended Rituximab Dosing Intervals in Multiple Sclerosis
    Chiara Starvaggi Cucuzza, Elisa Longinetti, Nicolas Ruffin, Björn Evertsson, Ingrid Kockum, Maja Jagodic, Faiez Al Nimer, Thomas Frisell, Fredrik Piehl
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    CD59 Expression in Skeletal Muscles and Its Role in Myasthenia Gravis
    Kazuo Iwasa, Yutaka Furukawa, Hiroaki Yoshikawa, Masahito Yamada, Kenjiro Ono
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Anti-Hu Antibodies in Patients With Neurologic Side Effects of Immune Checkpoint Inhibitors
    Antonio Farina, Macarena Villagrán-García, Nicolás Lundahl Ciano-Petersen, Alberto Vogrig, Sergio Muñiz-Castrillo, Luc Taillandier, Maud Michaud, Mathilde Lefilliatre, Adrien Wang, Zoe Lepine, Géraldine Picard, Valentin Wucher, Maroua Dhairi, Nicole Fabien, David Goncalves, Véronique Rogemond, Bastien Joubert, Jèrôme Honnorat
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    More Efficient Complement Activation by Anti–Aquaporin-4 Compared With Anti–Myelin Oligodendrocyte Glycoprotein Antibodies
    Magdalena Lerch, Kathrin Schanda, Eliott Lafon, Reinhard Würzner, Sara Mariotto, Alessandro Dinoto, Eva Maria Wendel, Christian Lechner, Harald Hegen, Kevin Rostásy, Thomas Berger, Doris Wilflingseder, Romana Höftberger, Markus Reindl
    • Abstract
    • Full Text
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  • Open Access
    Association of Vitamin D Polygenic Risk Scores and Disease Outcome in People With Multiple Sclerosis
    Eleni S. Vasileiou, Chen Hu, Charles N. Bernstein, Fred Lublin, Jerry S. Wolinsky, Gary R. Cutter, Elias S. Sotirchos, Kaarina Kowalec, Amber Salter, Shiv Saidha, Ellen M. Mowry, Peter A. Calabresi, Ruth Ann Marrie, Kathryn C. Fitzgerald
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Acute Inflammatory Diseases of the Central Nervous System After SARS-CoV-2 Vaccination
    Anna G. Francis, Kariem Elhadd, Valentina Camera, Monica Ferreira dos Santos, Chiara Rocchi, Poneh Adib-Samii, Bal Athwal, Kathrine Attfield, Andrew Barritt, Matthew Craner, Leonora Fisniku, Astrid K.N. Iversen, Oliver Leach, Lucy Matthews, Ian Redmond, Jonathan O'Riordan, Antonio Scalfari, Radu Tanasescu, Damian Wren, Saif Huda, Maria Isabel Leite, Lars Fugger, Jacqueline Palace
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Early Immunotherapy and Longer Corticosteroid Treatment Are Associated With Lower Risk of Relapsing Disease Course in Pediatric MOGAD
    Margherita Nosadini, Michael Eyre, Thea Giacomini, Massimiliano Valeriani, Marida Della Corte, Andrea D. Praticò, Pietro Annovazzi, Ramona Cordani, Duccio Maria Cordelli, Giovanni Crichiutti, Gabriella Di Rosa, Valentina Dolcemascolo, Anna Fetta, Elena Freri, Paolo Gallo, Matteo Gastaldi, Tiziana Granata, Luisa Grazian, Raffaele Iorio, Martina Lombardini, Monica Margoni, Sara Mariotto, Sara Matricardi, Federico Melani, Nardo Nardocci, Laura Papetti, Alice Passarini, Francesco Pisani, Chiara Po', Marco Puthenparampil, Francesca Ragona, Salvatore Savasta, Sabrina Siliquini, Irene Toldo, Alessandra Tozzo, Emanuela Claudia Turco, Antonio Varone, Alberto Vogrig, Luigi Zuliani, Samuela Bugin, Sara Rossato, Alessandro Orsini, Gaetano Cantalupo, Maria Margherita Mancardi, Michela Ada Noris Ferilli, Thomas Foiadelli, Stefano Sartori
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    miRNA Signature in CSF From Patients With Primary Progressive Multiple Sclerosis
    María Muñoz-San Martín, Imma Gómez, Ana Quiroga-Varela, Marina Gonzalez-del Río, René Robles Cedeño, Gary Álvarez, Maria Buxó, Albert Miguela, Luisa M. Villar, Jessica Castillo-Villalba, Bonaventura Casanova, Ester Quintana, Lluís Ramió-Torrentà
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Long-term Efficacy of Satralizumab in AQP4-IgG–Seropositive Neuromyelitis Optica Spectrum Disorder From SAkuraSky and SAkuraStar
    Ingo Kleiter, Anthony Traboulsee, Jacqueline Palace, Takashi Yamamura, Kazuo Fujihara, Albert Saiz, Adil Javed, David Mayes, H-Christian von Büdingen, Gaelle Klingelschmitt, Daniela Stokmaier, Jeffrey L. Bennett
    • Abstract
    • Full Text
    • Full Text (PDF)

Clinical/Scientific Notes

  • Open Access
    CLIPPERS Responsive to Cladribine as a Durable Steroid-Sparing Agent
    Simon Thebault, Hailey Bergman, Harold L. Atkins, Mark S. Freedman, John Brooks
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Immune-Mediated Rippling Muscle Disease Associated With Thymoma and Anti-MURC/Cavin-4 Autoantibodies
    Juliette Svahn, Laurent Coudert, Nathalie Streichenberger, Alexandra Kraut, Alice Gravier-Dumonceau-Mazelier, Ludivine Rotard, Laurence Calemard-Michel, Rita Menassa, Elisabeth Errazuriz-Cerda, Lara Chalabreysse, Alexis Osseni, Christophe Vial, Laurentiu Jomir, François Tronc, Do Le Duy, Emilien Bernard, Vincent Gache, Yohann Couté, Vincent Jacquemond, Laurent Schaeffer, Pascal Leblanc
    • Abstract
    • Full Text
    • Full Text (PDF)

Review

  • Open Access
    Secondary Progressive Multiple SclerosisA Review of Clinical Characteristics, Definition, Prognostic Tools, and Disease-Modifying Therapies
    Tjalf Ziemssen, Virender Bhan, Jeremy Chataway, Tanuja Chitnis, Bruce Anthony Campbell Cree, Eva Kubala Havrdova, Ludwig Kappos, Pierre Labauge, Aaron Miller, Jin Nakahara, Celia Oreja-Guevara, Jacqueline Palace, Barry Singer, Maria Trojano, Ashwini Patil, Benedict Rauser, Thomas Hach
    • Abstract
    • Full Text
    • Full Text (PDF)

Diagnostic & Treatment Challenges

  • Open Access
    Multiple Sclerosis Followed by Neuromyelitis Optica Spectrum DisorderFrom the National Multiple Sclerosis Society Case Conference Proceedings
    Carolyn Goldschmidt, Steven L. Galetta, Robert P. Lisak, Laura J. Balcer, Andrew Hellman, Michael K. Racke, Amy E. Lovett-Racke, Roberto Cruz, Matthew S. Parsons, Neda Sattarnezhad, Lawrence Steinman, Scott S. Zamvil, Elliot M. Frohman, Teresa C. Frohman
    • Abstract
    • Full Text
    • Full Text (PDF)
  • Open Access
    Recurrent Optic Neuritis and Perineuritis Followed by an Unexpected DiscoveryFrom the National Multiple Sclerosis Society Case Conference Proceedings
    Daniela A. Pimentel Maldonado, Robert Lisak, Steven Galetta, Laura Balcer, Thomas Varkey, Andrew Goodman, Jennifer Graves, Michael Racke, Scott S. Zamvil, Scott Newsome, Elliot M. Frohman, Teresa C. Frohman
    • Abstract
    • Full Text
    • Full Text (PDF)
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